| 别名 | ACADM;Medium-chain specific acyl-CoA dehydrogenase, mitochondrial;MCAD |
| 基因名称 | ACADM |
| 蛋白名称 | Medium-chain specific acyl-CoA dehydrogenase mitochondrial |
| 推荐应用 | |
| 反应物种 | Human,Mouse,Rat |
| 存储缓冲液 | PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA |
| Human Swissprot No. | P11310 |
| Mouse Gene ID | 11364 |
| Mouse Swissprot No. | P45952 |
| Rat Gene ID | 24158 |
| Rat Swissprot No. | P08503 |
| 特异性 | Endogenous |
| 稀释度 | IHC-P 1:500-1:2000, WB 1:2000-1:10000, IF 1:200-1:1000, ELISA 1:5000-1:20000 |
| 参考分子量 | 45kDa |
| 预测分子量 | 47kDa |
| 运输及保存条件 | Biological ice bag transportation. Store at -20°C for at least 12 months(Do not lower than -25°C). Avoid freeze/thaw cycles |
| 宿主 | Rabbit |
| 同种型 | IgG,Kappa |
| 背景介绍 | This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008], |
| 细胞定位 | Mitochondrion matrix . |
| Clonality | Monoclonal |
| 细胞定位 | Mitochondrion matrix . |
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